Cardiopulmonary bypass in hereditary spherocytosis: a case report
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چکیده
منابع مشابه
Cardiopulmonary bypass in hereditary spherocytosis: a case report.
Hereditary spherocytosis is a genetically determined abnormality of red blood cells. It is likely that a defect of intracellular glycolysis results in the formation of spherical cells (spherocytes) which have a reduced life span and exhibit increased osmotic fragility in hypotonic saline solutions, increased susceptibility to mechanical trauma, and spontaneous lysis on incubation. Lysis is mark...
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Hereditary spherocytosis (HS) is a familial hemolytic disorder with marked heterogeneity of clinical features, ranging from an asymptomatic condition to a fulminant hemolytic anemia. Although a positive family history of spherocytosis increases the risk for this disorder, it may be sporadic in some cases. In severe cases the disorder may be detected in early childhood, but in mild cases it may ...
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H EREDITARY SPHEROCYTOSIS in the Negro is a relatively rare occurrence. From a survey of the medical literature of the past 20 years, we have been able to collect 41 cases.1-’4 Some of these cases are subject to doubt as to whether they actually represent hereditary spherocytosis because of insufficient data or the presence of intercurrent disease.”12 It has been suggested by some authors that ...
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Paramyotonia congenita is a non-progressive disease characterised by myotonia (failure of muscle relaxation) induced by the exposure of the affected muscles to cold. Episodes of flaccid paralysis occur and may be related to hyperkalaemic periodic paralysis. Proximal myopathy or muscular hypertrophy may occur. The condition is inherited as an autosomal dominant.' Severe paralysis may occur with ...
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ژورنال
عنوان ژورنال: Thorax
سال: 1971
ISSN: 0040-6376
DOI: 10.1136/thx.26.1.131